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Cystic fibrosis medicines

You and your child should know the name and dose of each medicine your child is taking. Each person with CF may take different medicines, but this is a list of the ones most commonly used. Always make sure you have enough medicines on hand and use them as prescribed.

Bronchodilators

Brand name Generic name How does it work? Side effects
Proventil® HFA albuterol
  • Opens airways by relaxing the muscles around the airways
  • Shaky hands, "hyper" feeling, fast heartbeat, headache
Ventolin®
Xopenex® levalbuterol

 

Inhaled corticosteroids (Anti-inflammatory)

Brand name Generic name How does it work? Side effects
Flovent® fluticasone
  • Prevents or decreases swelling, inflammation, and mucus inside the airways

  • Hoarseness
  • Possible thrush; rinse mouth and spit after each use to prevent it


Pulmicort® budesonide
QVAR® beclomethasone
Asmanex® mometasone

 

Inhaled corticosteroids / Long-acting bronchodilators

Brand name Generic name How does it work? Side effects
Advair® fluticasone propionate and salmeterol
  • Prevents swelling, inflammation, and mucus inside the airways
  • Opens airways by relaxing muscles around them
  • Hoarseness
  • Possible thrush; rinse mouth and spit after each use to prevent it
Symbicort®

budesonide
and formoterol

Dulera®

mometasone and formoterol

 

Oral corticosteroids

Brand name Generic name How does it work? Side effects
Orapred® prednisolone

  • Decreases swelling, inflammation, and mucus inside the airways
  • Increased appetite, stomachache, mood changes, fluid retention, flushed face, perhaps temporary joint pain after it is stopped
Pediapred®
Prelone®
(various brands) prednisone

 

Mucolytic agents

Brand name Generic name How does it work? Side effects
Mucomyst® N-acetylcysteine
  • Decreases the thickness of lung secretions and loosens them from the lung walls
  • Improves airflow to the lungs and may decrease the risk of infection
  • Hoarseness, sore throat, rash
  • Nausea, vomiting, fast heartbeat, drowsiness
  • Cough, brochospasm
Pulmozyme® dornase alfa
 HyperSal®

hypertonic saline
(7%)

 

Antibiotics

Brand name Generic name How does it work? Side effects
Nebulized:
TOBI®
tobramycin
  • Prevents and treats infections
  • Attacks bacteria directly inside the airway
  • Voice changes
  • Cough, wheeze
  • Chest discomfort
Cayston® aztreonam
Colymycin® colistin sulfomethate
Oral - many types, such as:
  • Treats infections.
  • Distributed throughout the body
  • Stomach upset
  • Diarrhea
  • Yeast infections
  • Vein irritation with IVmedicines
Bactrim®

trimethoprim/
sulfamethoxazole

Cipro® ciprofloxacin
Keflex® cephalexin
Zithromax® azthromycin
Intravenous (IV) many types

 

Pancreatic enzymes

Brand name Generic name How does it work? Side effects
Creon® pancrelipase
  • Replaces missing digestive enzymes
  • Important: Do not use generic enzymes as they are broken down in stomach acid and are not effective
  • Nausea
  • Abdominal cramps
Pancreaze®
Pertyze®
Zenpep®
Ultrasa®
Viokace®

 

Gastrointestinal medicines

Brand name Generic name How does it work? Side effects
Aciphex® rabeprazole
  • Decreases the acidity of the stomach and small intestine to reduce heartburn
  • May improve the action of pancreatic enzymes
  • Upset stomach
  • Vomiting
  • Diarrhea
  • Headache
  • Dizziness
Nexium® esomperazole
Pepcid® famotidine
Prevacid® lansoprazole
Prilosec® omeprazole
Protonix® pantoprazole
Zantac® ranitidine
Actigall® ursodiol
  • Helps prevent and treat liver disease and gallstones by helping the liver metabolize fatty acids and bile
  • Rash
  • Fever
  • Allergic reaction

 

Nutritional supplement

Brand name Generic name How does it work? Side effects
ADEKs® vitamins
A, D, E, K

  • Supplements fat-soluble vitamins needed by the body
  • Nausea
  • Diarrhea
  • Dizziness
AquaADEKS®
Source CF®
Vitamax®
MVW®
Complete Formula®
Libertas®

 

Cystic Fibrosis Transmembrane Conductance Regulator Potentiator

Brand name Generic name How does it work? Side effects
Orkambi® lumacaftor/ivacaftor
  • Corrects the protein at the cell surface to allow the chloride and sodium (salt) to move in and out of the cell
  • Helps protein to fold so it can make it to the cell surface
  • Chest discomfort
  • Shortness of breath
  • Elevated liver function tests
Kalydeco® ivacaftor
  • Corrects the protein at the cell surface to allow the chloride and sodium (salt) to move in and out of the cell
  • Chest discomfort
  • Shortness of breath
  • Elevated liver function tests

 

Questions?

If you have any questions, please call the clinic or pharmacy.


Last reviewed 8/2015 ©Copyright

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This page is not specific to your child, but provides general information on the topic above. If you have any questions, please call your clinic. For more reading material about this and other health topics, please call or visit Children's Family Resource Center library, or visit www.childrensmn.org/educationmaterials.

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